Reddy, 2007: Overview of all reported HSP-SPAST patients

Index patient Sex Ethnicity Country of origin AAO AAE Family history Symptoms Initial symptoms Reported mutations
No
n.a.
USA
25
51
n.a.
Walking aids
Babinski sign
Spastic gait
Spasticity, lower limb
Hyperreflexia in upper limbs
-Pure or uncomplicated
Lower limb muscle weakness
Show more (+4)
n.a.
Yes
n.a.
USA
24
48
n.a.
-Pure or uncomplicated
Babinski sign
Hyperreflexia in upper limbs
Lower limb muscle weakness
Spasticity, lower limb
Spastic gait
Show more (+3)
n.a.
No
n.a.
USA
3
23
n.a.
Spastic gait
Hyperreflexia in upper limbs
Lower limb muscle weakness
Babinski sign
Spasticity, lower limb
-Pure or uncomplicated
Show more (+3)
n.a.